
14/04/2025
Treatment algorithm for Pulmonary Arterial Hypertension
Abbreviations: PAH: pulmonary arterial hypertension; IPAH: idiopathic PAH; HPAH: hereditary PAH; DT: drug and toxin; CTD:
connective tissue disease; ERA: endothelin-1 receptor antagonist; PDE-5i: phosphodiesterase-5 inhibitor; i.v.: intravenous; s.c.: subcutaneous; PPA:
prostacyclin pathway agent; sGCS: soluble guanylyl cyclase stimulator; Rx: prescription; mPAP: mean pulmonary artery pressure; PVR: pulmonary vascular resistance; FC: functional class; 6MWD: 6-min walk distance; RV: right ventricle.
Source: Chin KM, Gaine SP, Gerges C, et al. Treatment algorithm for pulmonary arterial
hypertension. Eur Respir J 2024; in press: 2401325 [DOI: 10.1183/13993003.01325-2024].