31/08/2023
A previously healthy 11-year-old girl presented to the emergency department with one day history of acute severe left lower abdominal pain and suprapubic pain. She also had nausea, anorexia and 2 episodes of vomiting. The pain was intermittent and severe, with prolonged duration than any similar attacks previously encountered, and it had not improved with simple pain killers. There was no dysuria, frequency, or urgency. She has started to menstruate regularly 6 months before. The patient gave a history of similar but less intense episodes of pain, about 4 months apart over the past four to five months. They each started just before menstruation time, mildly relieved by acetaminophen an. She had also noticedd that menstrual bleeding became more heavy. Her LMP was 10 days ago
Ultrasound:
Single Right kidney, normal in shape, echogenicity and corticomedullary differentiation with no renal stones or hydronephrosis.
Evidence of 2 uterine cavities noted,
The left uterine cavity is enlarged and containing blood, which extending down to the left va**na, which appears to be dilated as well, and compressing the empty right va**na.
The right uterine cavity is empty.
The right o***y looks normal.
The left o***y is enlarged measuring 4 cm in volume, containing multiple peripherally located follicles with positive color flow.
>>> Arising the possibility of intermittent Lt. ovarian torsion
Evidence of 4.7 x 3.7 cm hemorrhagic cyst arising from the left ova
The decision was made to send the patient for emergency exploration started by perineal exam which approve the presence of intrava**nal bulge to the left side with concomitant other va**nal opening .
Laparoscopic exam revealed: two uterus, Left Ovarian torsion, left large distal fallopian tube cyst
Final Diagnosis:
Herlyn Werner Wunderlich syndrome (HWWS) also documented as OBSTRUCTED HEMIVAGINA WITH IPSILATERAL RENAL ANOMALY (OHVIRA)