28/07/2024
TRUNCUS ARTERIOSUS (TYPE 4 A)images
TA occurs when the two main blood vessels arising from the heart — the aorta and the pulmonary artery — do not separate as they should during fetal development. Babies with TA are born with one large vessel, or “trunk,” exiting the heart instead of two separate ones.
In most cases, TA occurs with another congenital heart defect called ventricular septal defect (VSD). VSD is a hole in the wall between the heart’s two lower chambers.
runcus Arteriosus symptoms in infants may include:
Breathing problems
Cyanosis (bluish skin, lips and nails from not getting enough oxygen-rich blood)
Difficulty feeding
Fatigue or extreme sleepiness
Heart murmur (abnormal sounds in the heart)
Poor weight gain
Pounding heart
Weak pulse
Truncus Arteriosus Diagnosis
A doctor may diagnose TA before birth with a prenatal ultrasound. If clinicians notice symptoms of TA after birth, they may perform the following tests:
Cardiac catheterization
Chest X-ray
Echocardiogram (echo)
Electrocardiogram (ECG)
Pulse oximetry
Truncus Arteriosus Treatment
Babies with TA should have surgery within a few weeks after birth. Left untreated, TA can cause severe health complications or death because the amount of blood can overload the lungs while the oxygen level is too low.
Truncus arteriosus repair surgery
Truncus arteriosus repair involves the following steps:
Separating the pulmonary arteries from the aorta
Attaching the pulmonary arteries to the right ventricle using artificial tubes and valves
Repairing the trunk so it functions as a separate aorta
Applying a patch to close the ventricular septal defect
Some babies are not strong enough to have truncus arteriosus surgery right after birth. They may need special treatments for a few weeks until they are ready for the repair, such as:
Medication to help the heart pump blood more efficiently
Nutritional therapy, such as high-calorie formula, for weight gain
Tube feeding if the baby is too tired to bottle feed or breastfeed
Sometimes a smaller, temporary surgery can be done. During this surgery, a band is placed across the pulmonary artery to protect the lungs by managing the blood flow to the rest of the body. This can give the baby time to grow big enough to have a more lasting surgery.